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Narrowing of the dark valve: aortic stenosis in alkaptonuria

The commonest cardiac pathology in patients with alkaptonuria is aortic stenosis. Patients with alkaptonuria and aortic stenosis may remain asymptomatic until the 6th decade. Surgeons may have to deal with per-operative difficulties as alkaptonuria is a systemic disease. Proper preoperative planning...

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Dettagli Bibliografici
Pubblicato in:Indian J Thorac Cardiovasc Surg
Autori principali: Nagare, Ketak, Idhrees, Mohammed, Ibrahim, Mohammed, Jacob, Aju, Velayudhan, Bashi
Natura: Artigo
Lingua:Inglês
Pubblicazione: Springer Singapore 2020
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC8079573/
https://ncbi.nlm.nih.gov/pubmed/33967422
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s12055-020-01059-z
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