Carregant...

Heterozygous deletions of noncoding parts of the PRPF31 gene cause retinitis pigmentosa via reduced gene expression

PURPOSE: Heterozygous mutations in the gene PRPF31, encoding a pre-mRNA splicing factor, cause autosomal dominant retinitis pigmentosa (adRP) with reduced penetrance. At the molecular level, pathogenicity results from haploinsufficiency, as the largest majority of such mutations trigger nonsense-med...

Descripció completa

Guardat en:
Dades bibliogràfiques
Publicat a:Mol Vis
Autors principals: Ruberto, Francesco Paolo, Balzano, Sara, Namburi, Prasanthi, Kimchi, Adva, Pescini-Gobert, Rosanna, Obolensky, Alexey, Banin, Eyal, Ben-Yosef, Tamar, Sharon, Dror, Rivolta, Carlo
Format: Artigo
Idioma:Inglês
Publicat: Molecular Vision 2021
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC8056469/
https://ncbi.nlm.nih.gov/pubmed/33907366
Etiquetes: Afegir etiqueta
Sense etiquetes, Sigues el primer a etiquetar aquest registre!