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Adult onset type 2 familial hemophagocytic lymphohistiocytosis with PRF1 c.65delC/c.163C>T compound heterozygous mutations: A case report

BACKGROUND: Familial hemophagocytic lymphohistiocytosis (FHL) is a primary immunodefici-ency disease caused by gene defects. The onset of FHL in adolescents and adults may lead clinicians to ignore or even misdiagnose the disease. To the best of our knowledge, this is the first report to detail the...

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Detalhes bibliográficos
Publicado no:World J Clin Cases
Main Authors: Liu, Xin-Yi, Nie, Yan-Bo, Chen, Xue-Jing, Gao, Xiao-Hui, Zhai, Li-Jia, Min, Feng-Ling
Formato: Artigo
Idioma:Inglês
Publicado em: Baishideng Publishing Group Inc 2021
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC8026822/
https://ncbi.nlm.nih.gov/pubmed/33869605
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.12998/wjcc.v9.i10.2289
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