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Cellular and molecular mechanisms breaking immune tolerance in inborn errors of immunity

In addition to susceptibility to infections, conventional primary immunodeficiency disorders (PIDs) and inborn errors of immunity (IEI) can cause immune dysregulation, manifesting as lymphoproliferative and/or autoimmune disease. Autoimmunity can be the prominent phenotype of PIDs and commonly inclu...

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Detalles Bibliográficos
Publicado en:Cell Mol Immunol
Main Authors: Sogkas, Georgios, Atschekzei, Faranaz, Adriawan, Ignatius Ryan, Dubrowinskaja, Natalia, Witte, Torsten, Schmidt, Reinhold Ernst
Formato: Artigo
Idioma:Inglês
Publicado: Nature Publishing Group UK 2021
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC8015752/
https://ncbi.nlm.nih.gov/pubmed/33795850
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41423-020-00626-z
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