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Modulation of Ion Transport to Restore Airway Hydration in Cystic Fibrosis

Cystic fibrosis (CF) is a life-limiting genetic disorder caused by loss-of-function mutations in the gene which codes for the CF transmembrane conductance regulator (CFTR) Cl(−) channel. Loss of Cl(−) secretion across the apical membrane of airway lining epithelial cells results in dehydration of th...

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Publicat a:Genes (Basel)
Autors principals: Reihill, James A., Douglas, Lisa E. J., Martin, S. Lorraine
Format: Artigo
Idioma:Inglês
Publicat: MDPI 2021
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC8004921/
https://ncbi.nlm.nih.gov/pubmed/33810137
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/genes12030453
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