Protein Substitute Requirements of Patients with Phenylketonuria on BH4 Treatment: A Systematic Review and Meta-Analysis

The traditional treatment for phenylketonuria (PKU) is a phenylalanine (Phe)-restricted diet, supplemented with a Phe-free/low-Phe protein substitute. Pharmaceutical treatment with synthetic tetrahydrobiopterin (BH4), an enzyme cofactor, allows a patient subgroup to relax their diet. However, dietar...

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Bibliographic Details
Published in:Nutrients
Main Authors: Ilgaz, Fatma, Marsaux, Cyril, Pinto, Alex, Singh, Rani, Rohde, Carmen, Karabulut, Erdem, Gökmen-Özel, Hülya, Kuhn, Mirjam, MacDonald, Anita
Format: Artigo
Language:Inglês
Published: MDPI 2021
Subjects:
Review
Online Access:https://ncbi.nlm.nih.gov/pmc/articles/PMC8004763/
https://ncbi.nlm.nih.gov/pubmed/33807079
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/nu13031040
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