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Pre-clinical left ventricular myocardial remodeling in patients with Friedreich’s ataxia: A cardiac MRI study

BACKGROUND: Heart Failure (HF) is the most common cause of death in Friedreich’s ataxia (FRDA), an inherited mitochondrial disease. Myocardial fibrosis and myocardial hypertrophy are well-documented autopsy features among FRDA patients with HF. OBJECTIVES: To leverage the unique tissue characterizat...

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Publicat a:PLoS One
Autors principals: Takazaki, Karen A. G., Quinaglia, Thiago, Venancio, Thiago D., Martinez, Alberto R. M., Shah, Ravi V., Neilan, Tomas G., Jerosch-Herold, Michael, Coelho-Filho, Otávio R., França, Marcondes C.
Format: Artigo
Idioma:Inglês
Publicat: Public Library of Science 2021
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7996973/
https://ncbi.nlm.nih.gov/pubmed/33770103
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0246633
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