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Glomerulonephritis with severe nephrotic syndrome induced by immune complexes composed of galactose-deficient IgA1 in primary Sjögren’s syndrome: a case report

BACKGROUND: Primary Sjögren’s syndrome (pSS) is an auto-immune disease characterized by sialadenitis and dacryoadenitis with lymphoplasmacytic cell infiltration. In pSS, not only sicca symptoms, but also extra-glandular involvement induced by immune abnormalities based on pSS occurs. Renal involveme...

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Detalhes bibliográficos
Publicado no:BMC Nephrol
Main Authors: Nishioka, Ryo, Hara, Satoshi, Kawahara, Hiroyuki, Ito, Kiyoaki, Mizushima, Ichiro, Hirata, Masayoshi, Nagata, Michio, Kawano, Mitsuhiro
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2021
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7992980/
https://ncbi.nlm.nih.gov/pubmed/33765955
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12882-021-02306-0
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