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Erdheim-Chester Disease: MR Imaging, Anatomic, and Histopathologic Correlation of Orbital Involvement

Summary: Erdheim-Chester disease (ECD) is a rare form of histiocytosis of unknown origin characterized by tissue infiltration by lipid-laden histiocytes. Typically, the diaphyseal and metaphyseal portions of the tubular bones are affected, leading to a characteristic radiographic pattern of bone scl...

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Detalhes bibliográficos
Publicado no:AJNR Am J Neuroradiol
Main Authors: de Abreu, Marcelo R., Chung, Christine B., Biswal, Sandip, Haghighi, Parvis, Hesselink, John, Resnick, Donald
Formato: Artigo
Idioma:Inglês
Publicado em: American Society of Neuroradiology 2004
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7975611/
https://ncbi.nlm.nih.gov/pubmed/15090356
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