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MR Imaging and Proton MR Spectroscopy in Adult Krabbe Disease

Summary: We present the MR imaging findings in four patients (two pairs of siblings from two unrelated families) with adult Krabbe disease. In the first family, clinical presentation mimicked familial spastic paraplegia. Their MR images showed selective, increased signal intensity on T2-weighted seq...

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Detalhes bibliográficos
Publicado no:AJNR Am J Neuroradiol
Main Authors: Farina, Laura, Bizzi, Alberto, Finocchiaro, Gaetano, Pareyson, Davide, Sghirlanzoni, Angelo, Bertagnolio, Barbara, and Savoiardo, Mario, Naidu, and SakkuBai, Singhal, Bhim S., Wenger, David A.
Formato: Artigo
Idioma:Inglês
Publicado em: American Society of Neuroradiology 2000
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7974033/
https://ncbi.nlm.nih.gov/pubmed/11003282
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