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Whole Blood Thromboelastometry by ROTEM and Thrombin Generation by Genesia According to the Genotype and Clinical Phenotype in Congenital Fibrinogen Disorders

The outcome of congenital fibrinogen defects (CFD) is often unpredictable. Standard coagulation assays fail to predict the clinical phenotype. We aimed to assess the pheno- and genotypic associations of thrombin generation (TG) and ROTEM in CFD. We measured fibrinogen (Fg) activity and antigen, prot...

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Dades bibliogràfiques
Publicat a:Int J Mol Sci
Autors principals: Szanto, Timea, Lassila, Riitta, Lemponen, Marja, Lehtinen, Elina, Neerman-Arbez, Marguerite, Casini, Alessandro
Format: Artigo
Idioma:Inglês
Publicat: MDPI 2021
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7956597/
https://ncbi.nlm.nih.gov/pubmed/33668986
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms22052286
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