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Role of the DDX11 DNA Helicase in Warsaw Breakage Syndrome Etiology

Warsaw breakage syndrome (WABS) is a genetic disorder characterized by sister chromatid cohesion defects, growth retardation, microcephaly, hearing loss and other variable clinical manifestations. WABS is due to biallelic mutations of the gene coding for the super-family 2 DNA helicase DDX11/ChlR1,...

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Publicado en:Int J Mol Sci
Autores principales: Santos, Diana, Mahtab, Mohammad, Boavida, Ana, Pisani, Francesca M.
Formato: Artigo
Lenguaje:Inglês
Publicado: MDPI 2021
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC7956524/
https://ncbi.nlm.nih.gov/pubmed/33669056
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms22052308
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