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Isolated thoracic intramedullary Erdheim-Chester disease presenting with paraplegia: a case report and literature review

BACKGROUND: Erdheim-Chester disease (ECD) is a rare, idiopathic, systemic non-Langerhans cell histiocytosis involving long bone and visceral organs. Central nervous system (CNS) involvement is uncommon and most cases develop as a part of systemic disease. We present a rare case of variant ECD as an...

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Detalhes bibliográficos
Publicado no:BMC Musculoskelet Disord
Main Authors: Jeon, Ikchan, Choi, Joon Hyuk
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2021
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7955615/
https://ncbi.nlm.nih.gov/pubmed/33711983
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12891-021-04061-7
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