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Giant Hepatomegaly with Spleno-testicular Enlargement in a Patient with Apolipoprotein A-I Amyloidosis: An Uncommon Type of Amyloidosis in Japan

Hereditary systemic amyloidosis aside from transthyretin-related familial amyloid polyneuropathy is quite uncommon in Japan. We herein report a sporadic case of hereditary apolipoprotein A-I (apoAI) amyloidosis. The patient was a 43-year-old Japanese man who exhibited marked hepatomegaly with spleno...

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Detalhes bibliográficos
Publicado no:Intern Med
Main Authors: Yoshinaga, Tsuneaki, Katoh, Nagaaki, Yazaki, Masahide, Sato, Mitsuto, Kametani, Fuyuki, Yasuda, Hideo, Watanabe, Kyohei, Kawata, Kazuhito, Nakagawa, Mayuko, Sekijima, Yoshiki
Formato: Artigo
Idioma:Inglês
Publicado em: The Japanese Society of Internal Medicine 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7946490/
https://ncbi.nlm.nih.gov/pubmed/32999221
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2169/internalmedicine.5126-20
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