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Altered cytoskeletal arrangement in induced pluripotent stem cells and motor neurons from patients with riboflavin transporter deficiency

The cytoskeletal network plays a crucial role in the differentiation, morphogenesis, function and homeostasis of the nervous tissue, so that alterations in any of its components may lead to neurodegenerative diseases. Riboflavin transporter deficiency (RTD), a childhood-onset disorder characterized...

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Dettagli Bibliografici
Pubblicato in:Dis Model Mech
Autori principali: Niceforo, Alessia, Marioli, Chiara, Colasuonno, Fiorella, Petrini, Stefania, Massey, Keith, Tartaglia, Marco, Bertini, Enrico, Moreno, Sandra, Compagnucci, Claudia
Natura: Artigo
Lingua:Inglês
Pubblicazione: The Company of Biologists Ltd 2021
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7927654/
https://ncbi.nlm.nih.gov/pubmed/33468503
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1242/dmm.046391
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