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Cardiovascular phenotype of the Dmd(mdx) rat – a suitable animal model for Duchenne muscular dystrophy

Besides skeletal muscle abnormalities, Duchenne muscular dystrophy (DMD) patients present with dilated cardiomyopathy development, which considerably contributes to morbidity and mortality. Because the mechanisms responsible for the cardiac complications in the context of DMD are largely unknown, ev...

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Dettagli Bibliografici
Pubblicato in:Dis Model Mech
Autori principali: Szabó, Petra Lujza, Ebner, Janine, Koenig, Xaver, Hamza, Ouafa, Watzinger, Simon, Trojanek, Sandra, Abraham, Dietmar, Todt, Hannes, Kubista, Helmut, Schicker, Klaus, Remy, Séverine, Anegon, Ignacio, Kiss, Attila, Podesser, Bruno K., Hilber, Karlheinz
Natura: Artigo
Lingua:Inglês
Pubblicazione: The Company of Biologists Ltd 2021
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7927653/
https://ncbi.nlm.nih.gov/pubmed/33619211
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1242/dmm.047704
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