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Treatment with antifibrotic agents in idiopathic pleuroparenchymal fibroelastosis with usual interstitial pneumonia

BACKGROUND: There are no established therapeutic options available for idiopathic pleuroparenchymal fibroelastosis (IPPFE) apart from supportive care and lung transplantation. Furthermore, it is known that IPPFE with a usual interstitial pneumonia (UIP) pattern and lower lobe predominance is a disea...

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Detalhes bibliográficos
Publicado no:ERJ Open Res
Main Authors: Sugino, Keishi, Ono, Hirotaka, Shimizu, Hiroshige, Kurosawa, Takeyuki, Matsumoto, Keiko, Ando, Masahiro, Mori, Kiyoshi, Tsuboi, Eiyasu, Homma, Sakae, Kishi, Kazuma
Formato: Artigo
Idioma:Inglês
Publicado em: European Respiratory Society 2021
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7917230/
https://ncbi.nlm.nih.gov/pubmed/33681342
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1183/23120541.00196-2020
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