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MRI-visible perivascular spaces as an imaging biomarker in Fabry disease

INTRODUCTION: Fabry disease (FD) is an X-linked lysosomal storage disorder resulting in vascular glycosphingolipid accumulation and increased stroke risk. MRI findings associated with FD include white matter hyperintensities (WMH) and cerebral microbleeds (CMBs), suggesting the presence of cerebral...

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Detalhes bibliográficos
Publicado no:J Neurol
Main Authors: Lyndon, D., Davagnanam, I., Wilson, D., Jichi, F., Merwick, A., Bolsover, F., Jager, H. R., Cipolotti, L., Wheeler-Kingshott, C., Hughes, D., Murphy, E., Lachmann, R., Werring, D. J.
Formato: Artigo
Idioma:Inglês
Publicado em: Springer Berlin Heidelberg 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7914182/
https://ncbi.nlm.nih.gov/pubmed/33078310
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00415-020-10209-7
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