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Atypical Presentations of IPEX: Expect the Unexpected

Immune dysregulation, polyendocrinopathy, and enteropathy, X-linked (IPEX) syndrome is a rare disorder that has become a model of monogenic autoimmunity. IPEX is caused by mutations in FOXP3 gene, a master regulator of regulatory T cells (Treg). Cases reported in the last 20 years demonstrate that I...

Täydet tiedot

Tallennettuna:
Bibliografiset tiedot
Julkaisussa:Front Pediatr
Päätekijät: Consonni, Filippo, Ciullini Mannurita, Sara, Gambineri, Eleonora
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: Frontiers Media S.A. 2021
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC7892580/
https://ncbi.nlm.nih.gov/pubmed/33614561
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fped.2021.643094
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