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Inflammation and Fibrosis in Polycystic Kidney Disease

Polycystic kidney disease (PKD) is a commonly inherited disorder characterized by cyst formation and fibrosis (Wilson, N Engl J Med 350:151–164, 2004) and is caused by mutations in cilia or cilia-related proteins, such as polycystin 1 or 2 (Oh and Katsanis, Development 139:443–448, 2012; Kotsis et a...

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Detalhes bibliográficos
Publicado no:Results Probl Cell Differ
Main Authors: Song, Cheng Jack, Zimmerman, Kurt A., Henke, Scott J., Yoder, Bradley K.
Formato: Artigo
Idioma:Inglês
Publicado em: 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7875307/
https://ncbi.nlm.nih.gov/pubmed/28409351
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/978-3-319-51436-9_12
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