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Release of pseudosyndactyly in recessive dystrophic epidermolysis bullosa using a dermal regeneration template glove: the Foggia experience

BACKGROUND: Epidermolysis bullosa (EB) comprises a heterogeneous group of rare genetic diseases associated with skin blistering caused by minimal trauma. A major and common EB subtype, recessive dystrophic EB (RDEB), is characterized by altered wound healing, inflammatory dysbalance and fibrotic cha...

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Библиографические подробности
Опубликовано в: :Orphanet J Rare Dis
Главные авторы: Lembo, Fedele, Parisi, Domenico, Cecchino, Liberato Roberto, Ciancio, Francesco, Innocenti, Alessandro, Portincasa, Aurelio
Формат: Artigo
Язык:Inglês
Опубликовано: BioMed Central 2021
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC7845051/
https://ncbi.nlm.nih.gov/pubmed/33509245
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-021-01697-5
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