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Outcomes of Kidney Transplantation in Fabry Disease: A Meta-Analysis

Background: Fabry disease (FD) is a rare X-linked lysosomal storage disorder with progressive systemic deposition of globotriaosylceramide, leading to life-threatening cardiac, central nervous system, and kidney disease. Current therapy involves symptomatic medical management, enzyme replacement the...

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Bibliografiska uppgifter
I publikationen:Diseases
Huvudupphovsmän: Suarez, Maria L. Gonzalez, Thongprayoon, Charat, Hansrivijit, Panupong, Medaura, Juan, Vaitla, Pradeep, Mao, Michael A., Bathini, Tarun, Boonpheng, Boonphiphop, Kanduri, Swetha R., Kovvuru, Karthik, Basu, Arpita, Cheungpasitporn, Wisit
Materialtyp: Artigo
Språk:Inglês
Publicerad: MDPI 2020
Ämnen:
Länkar:https://ncbi.nlm.nih.gov/pmc/articles/PMC7838795/
https://ncbi.nlm.nih.gov/pubmed/33374610
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/diseases9010002
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