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Aortic Root Dilatation in Taiwanese Patients with Mucopolysaccharidoses and the Long-Term Effects of Enzyme Replacement Therapy

Background: Cardiovascular abnormalities have been observed in patients with mucopolysaccharidosis (MPS) of any type, with the most documented abnormalities being valvular regurgitation and stenosis and cardiac hypertrophy. Only a few studies have focused on aortic root dilatation and the long-term...

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Dades bibliogràfiques
Publicat a:Diagnostics (Basel)
Autors principals: Lin, Hsiang-Yu, Chen, Ming-Ren, Lee, Chung-Lin, Lin, Shan-Miao, Hung, Chung-Lieh, Niu, Dau-Ming, Chang, Tung-Ming, Chuang, Chih-Kuang, Lin, Shuan-Pei
Format: Artigo
Idioma:Inglês
Publicat: MDPI 2020
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7823494/
https://ncbi.nlm.nih.gov/pubmed/33374885
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/diagnostics11010016
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