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Cystic biliary atresia with congenital absence of portal vein

A 126-day female child presented with jaundice since day 7 of life. She was icteric and had hepatosplenomegaly. Radiological investigations revealed three extrahepatic and multiple intrahepatic biliary cysts, absent gall bladder and portal vein. These findings were confirmed on laparotomy. To the be...

Полное описание

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Библиографические подробности
Опубликовано в: :BMJ Case Rep
Главные авторы: Nandan, Ruchira, Jana, Manisha, Yadav, Devendra Kumar, Goel, Prabudh
Формат: Artigo
Язык:Inglês
Опубликовано: BMJ Publishing Group 2021
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC7813356/
https://ncbi.nlm.nih.gov/pubmed/33462044
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2020-239205
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