Chargement en cours...

Dysregulation of sonic hedgehog signaling causes hearing loss in ciliopathy mouse models

Defective primary cilia cause a range of diseases known as ciliopathies, including hearing loss. The etiology of hearing loss in ciliopathies, however, remains unclear. We analyzed cochleae from three ciliopathy mouse models exhibiting different ciliogenesis defects: Intraflagellar transport 88 (Ift...

Description complète

Enregistré dans:
Détails bibliographiques
Publié dans:eLife
Auteurs principaux: Moon, Kyeong-Hye, Ma, Ji-Hyun, Min, Hyehyun, Koo, Heiyeun, Kim, HongKyung, Ko, Hyuk Wan, Bok, Jinwoong
Format: Artigo
Langue:Inglês
Publié: eLife Sciences Publications, Ltd 2020
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7806262/
https://ncbi.nlm.nih.gov/pubmed/33382037
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.7554/eLife.56551
Tags: Ajouter un tag
Pas de tags, Soyez le premier à ajouter un tag!