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Intramuscular blood flow in Duchenne and Becker Muscular Dystrophy: quantitative power Doppler sonography relates to disease severity

OBJECTIVE: Absent or truncated dystrophin in Duchenne (DMD) and Becker (BMD) muscular dystrophies results in impaired vasodilatory pathways and exercise induced muscle ischemia. Here, we used power Doppler sonography to quantify changes in intramuscular blood flow immediately following exercise in b...

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Publicat a:Clin Neurophysiol
Autors principals: Dietz, Alexander R, Connolly, Anne, Dori, Amir, Zaidman, Craig M.
Format: Artigo
Idioma:Inglês
Publicat: 2019
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7798356/
https://ncbi.nlm.nih.gov/pubmed/31751835
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.clinph.2019.09.023
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