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Novel Therapeutic Approaches to Familial HLH (Emapalumab in FHL)
Primary Hemophagocytic lymphohistiocytosis (pHLH) is a rare, life-threatening, hyperinflammatory disorder, characterized by uncontrolled activation of the immune system. Mutations affecting several genes coding for proteins involved in the cytotoxicity machinery of both natural killer (NK) and T cel...
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| Izdano u: | Front Immunol |
|---|---|
| Glavni autori: | , , , |
| Format: | Artigo |
| Jezik: | Inglês |
| Izdano: |
Frontiers Media S.A.
2020
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| Teme: | |
| Online pristup: | https://ncbi.nlm.nih.gov/pmc/articles/PMC7793976/ https://ncbi.nlm.nih.gov/pubmed/33424859 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fimmu.2020.608492 |
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