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Leg ulceration with histological features of pseudoxanthoma elasticum

Pseudoxanthoma elasticum (PXE) is an inherited connective tissue disorder with extensive degeneration and calcification of elastic tissue. Histology demonstrates calcified elastic fibers in the mid to lower dermis with a characteristic “steel wool” appearance. A limited number of published cases hav...

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Détails bibliographiques
Publié dans:Proc (Bayl Univ Med Cent)
Auteurs principaux: Asad, Usman, Shah, Sheevam, Parekh, Palak
Format: Artigo
Langue:Inglês
Publié: Taylor & Francis 2020
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7785143/
https://ncbi.nlm.nih.gov/pubmed/33456154
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1080/08998280.2020.1826247
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