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Clinicopathologic and molecular features of intracranial desmoplastic small round cell tumors

Desmoplastic small round cell tumors (DSRCTs) are highly aggressive sarcomas that most commonly occur intra‐abdominally, and are defined by EWSR1‐WT1 gene fusion. Intracranial DSRCTs are exceptionally rare with only seven previously reported fusion‐positive cases. Herein, we evaluate the clinical, m...

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Detalhes bibliográficos
Publicado no:Brain Pathol
Main Authors: Lee, Julieann C., Villanueva‐Meyer, Javier E., Ferris, Sean P., Cham, Elaine M., Zucker, Jacob, Cooney, Tabitha, Gilani, Ahmed, Kleinschmidt‐DeMasters, Bette K., Trembath, Dimitri, Mafra, Manuela, Chiang, Jason, Ellison, David W., Cho, Soo‐Jin, Horvai, Andrew E., Van Ziffle, Jessica, Onodera, Courtney, Devine, Patrick, Grenert, James P., de Voijs, Carmen M.A., van Blokland, W.T. Marja, de Leng, Wendy W.J., Ploegmakers, Marieke J., Flucke, Uta, Pekmezci, Melike, Bollen, Andrew W., Tihan, Tarik, Koelsche, Christian, von Deimling, Andreas, Wesseling, Pieter, Solomon, David A., Perry, Arie
Formato: Artigo
Idioma:Inglês
Publicado em: John Wiley and Sons Inc. 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7780368/
https://ncbi.nlm.nih.gov/pubmed/31837177
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/bpa.12809
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