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M Mode Ultrasound and Tissue Doppler Imaging to Assess Diaphragm Feature in Late Onset Pompe Disease

Late-onset Pompe disease (LOPD) is an autosomal recessive lysosomal storage disease. Clinical features include skeletal muscle deficiency and diaphragm weakness. Clinical management relies on supportive treatment and mechanical ventilation in patients with chronic respiratory failure. M mode ultraso...

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Detalhes bibliográficos
Publicado no:Neurol Int
Main Authors: Meng, Paris, Ogna, Adam, Fayssoil, Abdallah
Formato: Artigo
Idioma:Inglês
Publicado em: MDPI 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7768541/
https://ncbi.nlm.nih.gov/pubmed/33203058
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/neurolint12030012
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