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Case Report: Secondary Hemophagocytic Lymphohistiocytosis With Disseminated Infection in Chronic Granulomatous Disease—A Serious Cause of Mortality

Chronic granulomatous disease (CGD) is a primary immune deficiency due to defects in phagocyte respiratory burst leading to severe and life-threatening infections. Patients with CGD also suffer from disorders of inflammation and immune dysregulation including colitis and granulomatous lung disease,...

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Détails bibliographiques
Publié dans:Front Immunol
Auteurs principaux: Squire, Jacqueline D., Vazquez, Stephanie N., Chan, Angela, Smith, Michele E., Chellapandian, Deepak, Vose, Laura, Teppa, Beatriz, Hanson, I. Celine, Chinn, Ivan K., Forbes-Satter, Lisa, Seeborg, Filiz O., Nicholas, Sarah K., Martinez, Caridad A., Allen, Carl E., Connors, Thomas J., Satwani, Prakash, Shtessel, Maria, Ale, Hanadys, Noroski, Lenora M., Rider, Nicholas L., Milner, Joshua D., Leiding, Jennifer W.
Format: Artigo
Langue:Inglês
Publié: Frontiers Media S.A. 2020
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7756012/
https://ncbi.nlm.nih.gov/pubmed/33362767
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fimmu.2020.581475
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