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Cytokine Signature in Schnitzler Syndrome: Proinflammatory Cytokine Production Associated to Th Suppression

BACKGROUND: Schnitzler syndrome (SchS) is a rare autoinflammatory disease characterized by urticarial exanthema, bone and joint alterations, fever and monoclonal IgM gammopathy. Overactivation of the interleukin(IL)-1 system is reported, even though the exact pathophysiological pathways remain unkno...

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Publicado en:Front Immunol
Main Authors: Masson Regnault, Marie, Frouin, Eric, Jéru, Isabelle, Delwail, Adriana, Charreau, Sandrine, Barbarot, Sébastien, Néel, Antoine, Masseau, Agathe, Puéchal, Xavier, Kyndt, Xavier, Gayet, Stephane, Lifermann, François, Asli, Bouchra, Balguerie, Xavier, Blanchard-Delaunay, Claire, Aubin, François, Rizzi, Rita, Rongioletti, Franco, Boyé, Thierry, Gusdorf, Laurence, Bessis, Didier, Morel, Franck, Hainaut, Ewa, Lipsker, Dan, Lecron, Jean-Claude
Formato: Artigo
Idioma:Inglês
Publicado: Frontiers Media S.A. 2020
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC7726442/
https://ncbi.nlm.nih.gov/pubmed/33324407
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fimmu.2020.588322
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