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High frequency of biotinidase deficiency in Italian population identified by newborn screening

The biotinidase (BTD) enzyme is essential for recycling biotin, a water-soluble B-complex vitamin that is the coenzyme of four carboxylases involved in fatty acid synthesis, amino acid catabolism and gluconeogenesis. If untreated, total or partial BTD deficiencies lead to an autosomal recessive inhe...

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書目詳細資料
發表在:Mol Genet Metab Rep
Main Authors: Funghini, Silvia, Tonin, Rodolfo, Malvagia, Sabrina, Caciotti, Anna, Donati, Maria Alice, Morrone, Amelia, la Marca, Giancarlo
格式: Artigo
語言:Inglês
出版: Elsevier 2020
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在線閱讀:https://ncbi.nlm.nih.gov/pmc/articles/PMC7719957/
https://ncbi.nlm.nih.gov/pubmed/33312878
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ymgmr.2020.100689
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