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Nutrient Intake and Nutritional Status in Adult Patients with Inherited Metabolic Diseases Treated with Low-Protein Diets: A Review on Urea Cycle Disorders and Branched Chain Organic Acidemias

Low-protein diets (LPDs) are the main treatment for urea cycle disorders (UCDs) and organic acidemias (OAs). In most cases, LPDs start in childhood and must be continued into adulthood. The improved life expectancy of patients with UCDs and OAs raises the question of their consequences on nutritiona...

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Detalhes bibliográficos
Publicado no:Nutrients
Main Authors: Francini-Pesenti, Francesco, Gugelmo, Giorgia, Lenzini, Livia, Vitturi, Nicola
Formato: Artigo
Idioma:Inglês
Publicado em: MDPI 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7693747/
https://ncbi.nlm.nih.gov/pubmed/33138136
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/nu12113331
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