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Brain MR Imaging Findings in Woodhouse-Sakati Syndrome

BACKGROUND AND PURPOSE: Woodhouse-Sakati syndrome is a rare autosomal recessive disorder characterized by hypogonadism, alopecia, diabetes mellitus, and progressive extrapyramidal signs. The disease is caused by biallelic pathogenic variants in the DCAF17 gene. The purpose of this study was to descr...

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Dettagli Bibliografici
Pubblicato in:AJNR Am J Neuroradiol
Autori principali: Abusrair, A.H., Bohlega, S., Al-Semari, A., Al-Ajlan, F.S., Al-Ahmadi, K., Mohamed, B., AlDakheel, A.
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society of Neuroradiology 2018
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7655421/
https://ncbi.nlm.nih.gov/pubmed/30409855
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3174/ajnr.A5879
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