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Excitability properties of mouse and human skeletal muscle fibres compared by muscle velocity recovery cycles

Mouse models of skeletal muscle channelopathies are not phenocopies of human disease. In some cases (e.g., Myotonia Congenita) the phenotype is much more severe, whilst in others (e.g. Hypokalaemic periodic paralysis) rodent physiology is protective. This suggests a species’ difference in muscle exc...

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Dettagli Bibliografici
Pubblicato in:Neuromuscul Disord
Autori principali: Suetterlin, K. J., Männikkö, R., Matthews, E., Greensmith, L., Hanna, M.G., Bostock, H., Tan, S.V.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2022
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7614892/
https://ncbi.nlm.nih.gov/pubmed/35339342
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.nmd.2022.02.011
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