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Proteins Structure Models in the Evaluation of Novel Variant (C.472_477del) in the MOCS2 Gene

(1) Background: Molybdenum cofactor deficiency type B (MOCODB, #252160) is a rare autosomal recessive metabolic disorder characterized by intractable seizures of neonatal-onset, muscular spasticity, accompanying with hypouricemia, elevated urinary sulfite levels and craniofacial dysmorphism. Thirty-...

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Dades bibliogràfiques
Publicat a:Diagnostics (Basel)
Autors principals: Jezela-Stanek, Aleksandra, Blaz, Witold, Gora, Artur, Bochenska, Malgorzata, Kusmierska, Katarzyna, Sykut-Cegielska, Jolanta
Format: Artigo
Idioma:Inglês
Publicat: MDPI 2020
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC7602273/
https://ncbi.nlm.nih.gov/pubmed/33066491
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/diagnostics10100821
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