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Negative bone scintigraphy in wild-type transthyretin cardiac amyloidosis

BACKGROUND: Amyloidosis is a rare systemic disease due to the extracellular tissue deposition of a fibrillar-shaped misfolded protein, called amyloid. Only two types of proteins commonly affect the heart leading to an infiltrative cardiomyopathy: immunoglobulin light chain and transthyretin (TTR) ca...

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Shranjeno v:
Bibliografske podrobnosti
izdano v:BMC Cardiovasc Disord
Main Authors: Martini, Nicolò, Rizzo, Stefania, Sarais, Cristiano, Cipriani, Alberto
Format: Artigo
Jezik:Inglês
Izdano: BioMed Central 2020
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC7596990/
https://ncbi.nlm.nih.gov/pubmed/33121442
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12872-020-01749-x
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