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Subcutaneous and transvenous implantable cardioverter defibrillator in high-risk long-QT syndrome type 3 associated with Val411Met mutation in SCN5A

Congenital long-QT syndrome type 3 (LQT3) with SCN5A-V411M mutation has been reported as a malignant case of LQT3 with highest risk for sudden cardiac death (SCD). Here, we present two cases of LQT3 with SCN5A-V411M who had been implanted with subcutaneous (S-) or transvenous (TV-) implantable cardi...

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Detalles Bibliográficos
Publicado en:J Cardiol Cases
Autores principales: Yokoyama, Yasuhiro, Aiba, Takeshi, Ueda, Nobuhiko, Nakajima, Kenzaburo, Kamakura, Tsukasa, Wada, Mitsuru, Yamagata, Kenichiro, Ishibashi, Kohei, Inoue, Yuko, Miyamoto, Koji, Nagase, Satoshi, Noda, Takashi, Yasuda, Satoshi, Shimizu, Wataru, Kusano, Kengo
Formato: Artigo
Lenguaje:Inglês
Publicado: Japanese College of Cardiology 2020
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC7588482/
https://ncbi.nlm.nih.gov/pubmed/33133318
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jccase.2020.07.007
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