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Microstructural damage of the cortico-striatal and thalamo-cortical fibers in Fabry disease: a diffusion MRI tractometry study

PURPOSE: Recent evidences have suggested the possible presence of an involvement of the extrapyramidal system in Fabry disease (FD), a rare X-linked lysosomal storage disorder. We aimed to investigate the microstructural integrity of the main tracts of the cortico-striatal-thalamo-cortical loop in F...

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Publicado en:Neuroradiology
Autores principales: Cocozza, Sirio, Schiavi, Simona, Pontillo, Giuseppe, Battocchio, Matteo, Riccio, Eleonora, Caccavallo, Simona, Russo, Camilla, Di Risi, Teodolinda, Pisani, Antonio, Daducci, Alessandro, Brunetti, Arturo
Formato: Artigo
Lenguaje:Inglês
Publicado: Springer Berlin Heidelberg 2020
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC7568710/
https://ncbi.nlm.nih.gov/pubmed/32700105
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00234-020-02497-7
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