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A case of classic galactosemia manifesting as neonatal early and profound indirect hyperbilirubinemia

Galactosemia is a rare autosomal recessive metabolic disorder that has three major types. The most common type is classic galactosemia. These patients have deficient galactose-1-phosphate-urydiltransferase. The enzyme deficiency often results in symptomatic disease if breastfeeding or lactose-contai...

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Detalhes bibliográficos
Publicado no:Turk Pediatri Ars
Main Authors: Kavehmanesh, Zohreh, Torkaman, Mohammad, Beiraghdar, Fatemeh
Formato: Artigo
Idioma:Inglês
Publicado em: Kare Publishing 2020
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7536454/
https://ncbi.nlm.nih.gov/pubmed/33061763
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.14744/TurkPediatriArs.2019.21298
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