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A CASE OF SOTOS SYNDROME CAUSED BY A NOVEL VARIANT IN THE NSD1 GENE: A PROPOSED RATIONALE TO TREAT ACCOMPANYING PRECOCIOUS PUBERTY

Sotos syndrome is characterized by overgrowth, macrocephaly, distinctive facial features, and learning disabilities and is associated with alterations in the nuclear receptor binding SET domain protein 1 (NSD1) gene. Due to the advanced bone age, the eventual adult height is usually at the upper lim...

Πλήρης περιγραφή

Αποθηκεύτηκε σε:
Λεπτομέρειες βιβλιογραφικής εγγραφής
Τόπος έκδοσης:Acta Endocrinol (Buchar)
Κύριοι συγγραφείς: Özcabi, B., Akay, G., Yesil, G., Uyur Yalcin, E., Kirmizibekmez, H.
Μορφή: Artigo
Γλώσσα:Inglês
Έκδοση: Acta Endocrinologica Foundation 2020
Θέματα:
Διαθέσιμο Online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7535889/
https://ncbi.nlm.nih.gov/pubmed/33029244
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4183/aeb.2020.245
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