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Skeletal muscle regeneration in facioscapulohumeral muscular dystrophy is correlated with pathological severity

Facioscapulohumeral muscular dystrophy (FSHD) is an autosomal-dominant myopathy characterized by slowly progressive skeletal muscle weakness and wasting. While a regenerative response is often provoked in many muscular dystrophies, little is known about whether a regenerative response is regularly e...

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Detalhes bibliográficos
Publicado no:Hum Mol Genet
Main Authors: Banerji, Christopher R S, Henderson, Don, Tawil, Rabi N, Zammit, Peter S
Formato: Artigo
Idioma:Inglês
Publicado em: Oxford University Press 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7530526/
https://ncbi.nlm.nih.gov/pubmed/32744322
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddaa164
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