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Embryonal rhabdomyosarcoma in a patient with a germline CBL pathogenic variant

Germline pathogenic variants in CBL are associated with an autosomal dominant RASopathy and an increased risk for malignancies, particularly juvenile myelomonocytic leukemia. Herein, we describe a patient with clinical features of a Noonan-spectrum disorder who developed embryonal rhabdomyosarcoma o...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Cancer Genet
Egile Nagusiak: Ji, Jianling, Navid, Fariba, Hiemenz, Mathew C., Kaneko, Maki, Zhou, Shengmei, Saitta, Sulagna C., Biegel, Jaclyn A.
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: 2018
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC7528629/
https://ncbi.nlm.nih.gov/pubmed/30803559
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.cancergen.2018.12.006
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