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Aortic root surgery in Marfan syndrome
Marfan syndrome (MFS) is an autosomal dominant connective disease etiologically related with FBN-1 gene mutation. The altered microfibril protein structure result in characteristic cardiovascular abnormalities including aortic root dilatation, aortic root aneurysms, and aortic dissections. Aortic ro...
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| Publicado no: | Indian J Thorac Cardiovasc Surg |
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| Main Authors: | , |
| Formato: | Artigo |
| Idioma: | Inglês |
| Publicado em: |
Springer Singapore
2018
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| Assuntos: | |
| Acesso em linha: | https://ncbi.nlm.nih.gov/pmc/articles/PMC7525511/ https://ncbi.nlm.nih.gov/pubmed/33061070 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s12055-018-0761-9 |
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