A carregar...

Maple Syrup Urine Disease Masquerading as Urea Cycle Disorder: A Tale of Two Clinical Mimics

Maple syrup urine disease, an inherited disorder of metabolism, is characterised by deficient activity of the branched-chain alpha-keto acid dehydrogenase complex (BCKAD) enzyme, resulting in an accumulation of branched-chain amino acids. While it is classically diagnosed by the means of a neonatal...

ver descrição completa

Na minha lista:
Detalhes bibliográficos
Publicado no:Cureus
Main Authors: Rauf, Shahzad, Almas, Talal, Ullah, Irfan, Usman, Norina, Irfan, Muhammad
Formato: Artigo
Idioma:Inglês
Publicado em: Cureus 2020
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7489313/
https://ncbi.nlm.nih.gov/pubmed/32944429
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.7759/cureus.9706
Tags: Adicionar Tag
Sem tags, seja o primeiro a adicionar uma tag!