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Natural variation in a glucuronosyltransferase modulates propionate sensitivity in a C. elegans propionic acidemia model

Mutations in human metabolic genes can lead to rare diseases known as inborn errors of human metabolism. For instance, patients with loss-of-function mutations in either subunit of propionyl-CoA carboxylase suffer from propionic acidemia because they cannot catabolize propionate, leading to its harm...

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Detalhes bibliográficos
Publicado no:PLoS Genet
Main Authors: Na, Huimin, Zdraljevic, Stefan, Tanny, Robyn E., Walhout, Albertha J. M., Andersen, Erik C.
Formato: Artigo
Idioma:Inglês
Publicado em: Public Library of Science 2020
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7482840/
https://ncbi.nlm.nih.gov/pubmed/32857789
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pgen.1008984
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