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BDK Deficiency in Cerebral Cortex Neurons Causes Neurological Abnormalities and Affects Endurance Capacity

Branched-chain amino acid (BCAA) catabolism is regulated by its rate-limiting enzyme, branched-chain α-keto acid dehydrogenase (BCKDH), which is negatively regulated by BCKDH kinase (BDK). Loss of BDK function in mice and humans leads to dysregulated BCAA catabolism accompanied by neurological sympt...

Täydet tiedot

Tallennettuna:
Bibliografiset tiedot
Julkaisussa:Nutrients
Päätekijät: Mizusawa, Anna, Watanabe, Ayako, Yamada, Minori, Kamei, Rina, Shimomura, Yoshiharu, Kitaura, Yasuyuki
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: MDPI 2020
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC7469005/
https://ncbi.nlm.nih.gov/pubmed/32751134
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/nu12082267
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