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T-Cell Immunodeficiencies With Congenital Alterations of Thymic Development: Genes Implicated and Differential Immunological and Clinical Features

Combined Immunodeficiencies (CID) are rare congenital disorders characterized by defective T-cell development that may be associated with B- and NK-cell deficiency. They are usually due to alterations in genes expressed in hematopoietic precursors but in few cases, they are caused by impaired thymic...

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Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Cyhoeddwyd yn:Front Immunol
Prif Awduron: Giardino, Giuliana, Borzacchiello, Carla, De Luca, Martina, Romano, Roberta, Prencipe, Rosaria, Cirillo, Emilia, Pignata, Claudio
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: Frontiers Media S.A. 2020
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC7457079/
https://ncbi.nlm.nih.gov/pubmed/32922396
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fimmu.2020.01837
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