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Higher dietary protein intake preserves lean body mass, lowers liver lipid deposition, and maintains metabolic control in participants with long-chain fatty acid oxidation disorders

Medical nutrition therapy for long-chain fatty acid oxidation disorders (LC-FAODs) currently emphasizes fasting avoidance, restricted dietary long-chain fatty acid intake, supplementation with medium chain triglycerides, and increased carbohydrate intake. We hypothesize that increasing dietary prote...

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Detalhes bibliográficos
Publicado no:J Inherit Metab Dis
Main Authors: Gillingham, Melanie B., Elizondo, Gabriela, Behrend, Annie, Matern, Dietrich, Schoeller, Dale A., Harding, Cary O., Purnell, Jonathan Q.
Formato: Artigo
Idioma:Inglês
Publicado em: 2019
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7452215/
https://ncbi.nlm.nih.gov/pubmed/31295363
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jimd.12155
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